HMBS Antibody - C-terminal region : FITC (ARP74562_P050-FITC)
Product Specifications
Gene Name
Hydroxymethylbilane synthase
Gene Aliases
UPS, PBGD, PORC, PBG-D
Gene ID
3145
Swiss Prot
P08397
Host
Rabbit
Reactivity
Human
Immunogen
The immunogen is a synthetic peptide directed towards the C-terminal region of Human HEM3
Target
This gene encodes a member of the hydroxymethylbilane synthase superfamily. The encoded protein is the third enzyme of the heme biosynthetic pathway and catalyzes the head to tail condensation of four porphobilinogen molecules into the linear hydroxymethylbilane. Mutations in this gene are associated with the autosomal dominant disease acute intermittent porphyria. Alternatively spliced transcript variants encoding different isoforms have been described.
Partner Proteins
RANBP9; APP; UBC
Clonality
Polyclonal
Conjugation
FITC: Fluorescein Isothiocyanate
Type
Polyclonal Antibody
Applications
WB
Purification
Affinity Purified
Concentration
0.5 mg/ml
Format
Liquid. Purified antibody supplied in 1x PBS buffer.
Reconstitution
All conjugated antibodies should be stored in light-protected vials or covered with a light protecting material (i.e. aluminum foil) . Conjugated antibodies are stable for at least 12 months at 4C. If longer storage is desired (24 months), conjugates may be diluted with up to 50% glycerol and stored at -20C to -80C. Freezing and thawing conjugated antibodies will compromise enzyme activity as well as antibody binding.
Molecular Weight
39kDa
Shipping Conditions
Wet Ice
Product Datasheet
Anti-HMBS (ARP74562_P050-FITC) antibody
Protein Length
361
NCBI Gene Symbol
HMBS
NCBI GB Accession Number
HMBS
Host or Source
Rabbit
Protein Name
Porphobilinogen deaminase
Peptide Sequence
VPAQHEDGPEDDPQLVGITARNIPRGPQLAAQNLGISLANLLLSKGAKNI
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