D2HGDH Antibody - C-terminal region : FITC (ARP66551_P050-FITC)
Selected Variant
ARP66551_P050-FITC
Size: 100 µL
Product Specifications
Gene Aliases
D2HGD
Gene ID
728294
Swiss Prot
Q8N465
Accession Number
NP_689996
Host
Rabbit
Reactivity
Human, Mouse, Rat, Dog, Horse, Pig, Rabbit
Immunogen
The immunogen is a synthetic peptide directed towards the C-terminal region of Human D2HGDH
Target
This gene encodes D-2hydroxyglutarate dehydrogenase, a mitochondrial enzyme belonging to the FAD-binding oxidoreductase/transferase type 4 family. This enzyme, which is most active in liver and kidney but also active in heart and brain, converts D-2-hydroxyglutarate to 2-ketoglutarate. Mutations in this gene are present in D-2-hydroxyglutaric aciduria, a rare recessive neurometabolic disorder causing developmental delay, epilepsy, hypotonia, and dysmorphic features.
Partner Proteins
SUMO1; UBC
Clonality
Polyclonal
Conjugation
FITC: Fluorescein Isothiocyanate
Type
Polyclonal Antibody
Applications
WB
Purification
Affinity Purified
Concentration
0.5 mg/ml
Homology
Dog: 79%; Horse: 86%; Human: 100%; Mouse: 100%; Pig: 77%; Rabbit: 100%; Rat: 92%
Format
Liquid. Purified antibody supplied in 1x PBS buffer.
Reconstitution
All conjugated antibodies should be stored in light-protected vials or covered with a light protecting material (i.e. aluminum foil) . Conjugated antibodies are stable for at least 12 months at 4C. If longer storage is desired (24 months), conjugates may be diluted with up to 50% glycerol and stored at -20C to -80C. Freezing and thawing conjugated antibodies will compromise enzyme activity as well as antibody binding.
Molecular Weight
55kDa
Shipping Conditions
Wet Ice
Protein Length
521
NCBI Gene Symbol
D2HGDH
NCBI GB Accession Number
D2HGDH
Host or Source
Rabbit
Protein Name
D-2-hydroxyglutarate dehydrogenase, mitochondrial
Nucleotide Accession Number
NM_152783
Peptide Sequence
QESPFYVLIETSGSNAGHDAEKLGHFLEHALGSGLVTDGTMATDQRKVKM
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