GBE1 Antibody - N-terminal region : FITC (ARP64504_P050-FITC)
Product Specifications
Gene Name
Glucan (1,4-alpha-), branching enzyme 1
Gene Aliases
GBE, APBD, GSD4
Gene ID
2632
Swiss Prot
Q04446
Accession Number
NP_000149
Host
Rabbit
Reactivity
Human, Mouse, Rat, Cow, Dog, Guinea Pig, Horse, Rabbit
Target
The protein encoded by this gene is a glycogen branching enzyme that catalyzes the transfer of alpha-1,4-linked glucosyl units from the outer end of a glycogen chain to an alpha-1,6 position on the same or a neighboring glycogen chain. Branching of the chains is essential to increase the solubility of the glycogen molecule and, consequently, in reducing the osmotic pressure within cells. Highest level of this enzyme are found in liver and muscle. Mutations in this gene are associated with glycogen storage disease IV (also known as Andersen's disease) .
Partner Proteins
UBC; SUMO1; NEDD8; PRMT6; EPHB3; TRDMT1; DAK; UBD; ELAVL1; SUMO2; PGD
Clonality
Polyclonal
Conjugation
FITC: Fluorescein Isothiocyanate
Type
Polyclonal Antibody
Applications
WB
Purification
Affinity Purified
Concentration
0.5 mg/ml
Homology
Cow: 83%; Dog: 83%; Guinea Pig: 85%; Horse: 92%; Human: 100%; Mouse: 92%; Rabbit: 92%; Rat: 92%
Format
Liquid. Purified antibody supplied in 1x PBS buffer.
Reconstitution
All conjugated antibodies should be stored in light-protected vials or covered with a light protecting material (i.e. aluminum foil) . Conjugated antibodies are stable for at least 12 months at 4C. If longer storage is desired (24 months), conjugates may be diluted with up to 50% glycerol and stored at -20C to -80C. Freezing and thawing conjugated antibodies will compromise enzyme activity as well as antibody binding.
Molecular Weight
80kDa
Shipping Conditions
Wet Ice
Product Datasheet
Anti-GBE1 (ARP64504_P050-FITC) antibody
Protein Length
702
NCBI Gene Symbol
GBE1
NCBI GB Accession Number
GBE1
Host or Source
Rabbit
Protein Name
1,4-alpha-glucan-branching enzyme
Nucleotide Accession Number
NM_000158
Peptide Sequence
IHWDPEHSYEFKHSRPKKPRSLRIYESHVGISSHEGKVASYKHFTCNVLP
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