PPOX Antibody - N-terminal region : FITC (ARP56095_P050-FITC)
Selected Variant
ARP56095_P050-FITC
Size: 100 µL
Product Specifications
Gene Name
Protoporphyrinogen oxidase
Gene Aliases
VP, PPO, V290M
Gene ID
5498
Swiss Prot
P50336
Accession Number
NP_000300
Host
Rabbit
Reactivity
Human, Mouse, Rat, Cow, Dog, Guinea Pig, Horse, Pig, Rabbit
Immunogen
The immunogen is a synthetic peptide directed towards the N terminal region of human PPOX
Target
PPOX catalyzes the 6-electron oxidation of protoporphyrinogen-IX to form protoporphyrin-IX..This gene encodes the penultimate enzyme of heme biosynthesis, which catalyzes the 6-electron oxidation of protoporphyrinogen IX to form protoporphyrin IX. Mutations in this gene cause variegate porphyria, an autosomal dominant disorder of heme metabolism resulting from a deficiency in protoporphyrinogen oxidase, an enzyme located on the inner mitochondrial membrane. Alternatively spliced transcript variants encoding the same protein have been identified.
Partner Proteins
HNRNPD; UBC; COPS5; HAP1; PPOX; IMMT
Clonality
Polyclonal
Conjugation
FITC: Fluorescein Isothiocyanate
Type
Polyclonal Antibody
Applications
WB
Purification
Affinity Purified
Concentration
0.5 mg/ml
Homology
Cow: 100%; Dog: 93%; Guinea Pig: 86%; Horse: 100%; Human: 100%; Mouse: 100%; Pig: 100%; Rabbit: 100%; Rat: 100%
Format
Liquid. Purified antibody supplied in 1x PBS buffer.
Reconstitution
All conjugated antibodies should be stored in light-protected vials or covered with a light protecting material (i.e. aluminum foil) . Conjugated antibodies are stable for at least 12 months at 4C. If longer storage is desired (24 months), conjugates may be diluted with up to 50% glycerol and stored at -20C to -80C. Freezing and thawing conjugated antibodies will compromise enzyme activity as well as antibody binding.
Molecular Weight
51kDa
References & Citations
De Gene 409 (1-2), 83-91 (2008)
Shipping Conditions
Wet Ice
Protein Length
477
NCBI Gene Symbol
PPOX
NCBI GB Accession Number
PPOX
Host or Source
Rabbit
Protein Name
Protoporphyrinogen oxidase
Nucleotide Accession Number
NM_000309
Peptide Sequence
SSERLGGWIRSVRGPNGAIFELGPRGIRPAGALGARTLLLVSELGLDSEV
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