SGSH Antibody - C-terminal region : FITC (ARP48124_P050-FITC)
Selected Variant
ARP48124_P050-FITC
Size: 100 µL
Product Specifications
Gene Name
N-sulfoglucosamine sulfohydrolase
Gene Aliases
HSS, SFMD, MPS3A
Gene ID
6448
Swiss Prot
P51688
Accession Number
NP_000190.1
Host
Rabbit
Reactivity
Human, Mouse, Rat, Cow, Dog, Horse
Immunogen
The immunogen is a synthetic peptide directed towards the C-terminal region of human SGSH
Target
This gene encodes one of several enzymes involved in the lysosomal degradation of heparan sulfate. Mutations in this gene are associated with Sanfilippo syndrome A, one type of the lysosomal storage disease mucopolysaccaridosis III, which results from impaired degradation of heparan sulfate. Transcripts of varying sizes have been reported but their biological validity has not been determined.
Clonality
Polyclonal
Conjugation
FITC: Fluorescein Isothiocyanate
Type
Polyclonal Antibody
Applications
WB
Purification
Affinity Purified
Concentration
0.5 mg/ml
Homology
Cow: 79%; Dog: 86%; Horse: 93%; Human: 100%; Mouse: 79%; Rat: 79%
Format
Liquid. Purified antibody supplied in 1x PBS buffer.
Reconstitution
All conjugated antibodies should be stored in light-protected vials or covered with a light protecting material (i.e. aluminum foil) . Conjugated antibodies are stable for at least 12 months at 4C. If longer storage is desired (24 months), conjugates may be diluted with up to 50% glycerol and stored at -20C to -80C. Freezing and thawing conjugated antibodies will compromise enzyme activity as well as antibody binding.
Molecular Weight
32kDa
Shipping Conditions
Wet Ice
Protein Length
299
NCBI Gene Symbol
SGSH
NCBI GB Accession Number
SGSH
Host or Source
Rabbit
Protein Name
N-sulphoglucosamine sulphohydrolase
Nucleotide Accession Number
NM_000199.3
Peptide Sequence
ARWELYDRSRDPHETQNLATDPRFAQLLEMLRDQLAKWQWETHDPWVCAP
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