Welcome to GenPrice! Check out our latest updates.

Shopping Cart (0)

Your cart is empty

Add some products to get started!

GAA Antibody : HRP (ARP44227_P050-HRP)

Selected Variant

ARP44227_P050-HRP

Size: 100 µL

Product Specifications

Gene Name

Glucosidase, alpha; acid

Gene Aliases

LYAG

Gene ID

2548

Swiss Prot

P10253

Accession Number

NP_000143

Host

Rabbit

Reactivity

Human, Mouse, Rat, Cow, Dog, Guinea Pig, Horse

Immunogen

The immunogen is a synthetic peptide directed towards the following sequence APTPGANLYGSHPFYLALEDGGSAHGVFLLNSNAMDVVLQPSPALSWRST

Target

This gene encodes acid alpha-glucosidase, which is essential for the degradation of glycogen to glucose in lysosomes. Different forms of acid alpha-glucosidase are obtained by proteolytic processing. Defects in this gene are the cause of glycogen storage disease II, also known as Pompe's disease, which is an autosomal recessive disorder with a broad clinical spectrum. Three transcript variants encoding the same protein have been found for this gene.

Partner Proteins

UBC; SUMO1; NEDD8; NUMBL; STAT2; HIVEP1; EP300; SYNCRIP; MTHFD1; ILF3; HNRNPK; CDH2; CALU; FBXO6; NCF1

Clonality

Polyclonal

Conjugation

HRP: Horseradish Peroxidase

Type

Polyclonal Antibody

Purification

Affinity Purified

Concentration

0.5 mg/ml

Homology

Cow: 92%; Dog: 100%; Guinea Pig: 100%; Horse: 93%; Human: 100%; Mouse: 100%; Rat: 100%

Format

Liquid. Purified antibody is supplied in high phosphate PBS, 100 mm phosphate, 150 mM NaCl, pH 7.6.

Reconstitution

All conjugated antibodies should be stored in light-protected vials or covered with a light protecting material (i.e. aluminum foil) . Conjugated antibodies are stable for at least 12 months at 4C. If longer storage is desired (24 months), conjugates may be diluted with up to 50% glycerol and stored at -20C to -80C. Freezing and thawing conjugated antibodies will compromise enzyme activity as well as antibody binding.

Molecular Weight

105 kDa

Shipping Conditions

Wet Ice

Protein Length

952

NCBI Gene Symbol

GAA

NCBI GB Accession Number

GAA

Host or Source

Rabbit

Protein Name

Lysosomal alpha-glucosidase

Nucleotide Accession Number

NM_000152

Peptide Sequence

APTPGANLYGSHPFYLALEDGGSAHGVFLLNSNAMDVVLQPSPALSWRST

Price

Sign In for Pricing

Frequently Asked Questions

More Discoveries

Explore Other Products

Browse additional items from our catalog

Anti-Moesin/MSN Antibody Picoband®
A00766-1 100 µg/Vial

Anti-Moesin/MSN Antibody Picoband®

Sign In for Pricing
View Details
Phospho-Glycogen synthase 1 (S641) Recombinant Rabbit Monoclonal Antibody [SR46-06]
ET1602-13 100 µL

Phospho-Glycogen synthase 1 (S641) Recombinant Rabbit Monoclonal Antibody [SR46-06]

Sign In for Pricing
View Details
Bcl-2 (124), 0.2mg/mL
BNUB0530-500 1x 500 µL

Bcl-2 (124), 0.2mg/mL

Sign In for Pricing
View Details
Desmoglein-3 (Squamous Cell Marker) (DSG3/2839), CF647 conjugate, 0.1mg/mL
BNC472839-500 1x 500 µL

Desmoglein-3 (Squamous Cell Marker) (DSG3/2839), CF647 conjugate, 0.1mg/mL

Sign In for Pricing
View Details
GATA-3 (Breast and Urothelial Marker) (GATA3/2445), CF594 conjugate, 0.1mg/mL
BNC942445-100 1x 100 µL

GATA-3 (Breast and Urothelial Marker) (GATA3/2445), CF594 conjugate, 0.1mg/mL

Sign In for Pricing
View Details
Anti-HEXA Antibody Picoband®, APC Conjugate
PA1787-APC 100 µg/Vial

Anti-HEXA Antibody Picoband®, APC Conjugate

Sign In for Pricing
View Details