4-Methylumbelliferyl 2-sulfamino-2-deoxy-α-D-Glucopyranoside (sodium salt)

4-Methylumbelliferyl 2-sulfamino-2-deoxy-α-D-Glucopyranoside (4-MU-α-GlcNS) is a fluorogenic substrate for the enzyme heparin sulphamidase. Its sequential enzymatic cleavage ultimately releases fluorescent 4-methylumbelliferone (4-MU), enabling the in vitro quantification of enzyme activity for diagnosing lysosomal storage disorders like Mucopolysaccharidosis IIIA (Sanfilippo syndrome A) .