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3-Hydroxyisovalerylcarnitine

3-Hydroxyisovalerylcarnitine is a biomarker for biotin deficiency, as its elevated plasma levels indicate impaired leucine catabolism due to reduced 3-methylcrotonyl-CoA carboxylase activity. This small molecule is utilized in research applications involving metabolic disorder studies, biomarker validation, and in vitro diagnostic assay development.

Product Specifications

CAS Number

99159-87-2

Field of Research

Metabolism Research

Smiles

O ([C@@H] (C[N+] (C) (C) C) CC ([O-]) =O) C (CC (C) (C) O) =O

Molecular Formula

C12H23NO5

Molecular Weight

261.32

Storage Conditions

-20°C

Notes

For research use only.

Available Sizes

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