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3β,5α,6β-Trihydroxycholanic Acid

3β,5α,6β-Trihydroxycholanic acid is a bile acid derivative found at elevated levels in the dried blood spots of Niemann-Pick disease type C (NPC) patients. This metabolite serves as a potential biomarker for researching NPC pathogenesis and for evaluating therapeutic interventions in both cellular and animal models of this lysosomal storage disorder.

Product Specifications

CAS Number

16030-92-5

Field of Research

Metabolism Research

Smiles

C[C@@]12[C@@]3 ([C@] ([C@]4 ([C@] (C) (CC3) [C@@] ([C@@H] (CCC (O) =O) C) (CC4) [H]) [H]) (C[C@@H] (O) [C@@]1 (O) C[C@@H] (O) CC2) [H]) [H]

Molecular Formula

C24H40O5

Molecular Weight

408.6

Storage Conditions

-20°C

Notes

For research use only.

Available Sizes

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