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Glutarylcarnitine

Glutarylcarnitine is a key diagnostic biomarker for glutaric aciduria type I and malonic aciduria, routinely detected in newborn screening. This acylcarnitine is utilized in research to study inborn errors of metabolism, serving as a reference standard for both in vitro diagnostic assay development and metabolic pathway investigations.

Product Specifications

CAS Number

102636-82-8

Product Name Alternative

O-glutaroyl-L-carnitine, Endogenous Metabolite, EndogenousMetabolite, Glutarylcarnitine, Human Endogenous Metabolite

Field of Research

Metabolism Research

Purity

99.00% (May vary between batches)

Smiles

[C@H] (OC (CCCC (O) =O) =O) (C[N+] (C) (C) C) CC ([O-]) =O

Molecular Formula

C12H21NO6

Molecular Weight

275.3

Storage Conditions

-20°C

Notes

For research use only.

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