Glutarylcarnitine
Glutarylcarnitine is a key diagnostic biomarker for glutaric aciduria type I and malonic aciduria, routinely detected in newborn screening. This acylcarnitine is utilized in research to study inborn errors of metabolism, serving as a reference standard for both in vitro diagnostic assay development and metabolic pathway investigations.
Product Specifications
CAS Number
102636-82-8
Product Name Alternative
O-glutaroyl-L-carnitine, Endogenous Metabolite, EndogenousMetabolite, Glutarylcarnitine, Human Endogenous Metabolite
Field of Research
Metabolism Research
Purity
99.00% (May vary between batches)
Smiles
[C@H] (OC (CCCC (O) =O) =O) (C[N+] (C) (C) C) CC ([O-]) =O
Molecular Formula
C12H21NO6
Molecular Weight
275.3
Storage Conditions
-20°C
Notes
For research use only.
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