Isobutyryl Coenzyme A (sodium salt)

Isobutyryl-CoA is a short-chain branched acyl-CoA ester that serves as a substrate for isobutyryl-CoA dehydrogenase in valine catabolism. It is a key intermediate in studies of inborn errors of metabolism, such as IBDH deficiency, where it leads to the accumulation of isobutyryl-L-carnitine in both in vitro and in vivo research models.