3-Methyl-2-oxobutanoic acid
3-Methyl-2-oxobutanoic acid (2-Oxoisovaleric acid) is a neurotoxic keto-acid metabolite from incomplete branched-chain amino acid catabolism, leading to organic acidemias. It is used in research models of maple syrup urine disease (MSUD) to study metabolic acidosis and neurotoxicity in vitro and in vivo.
Product Specifications
CAS Number
759-05-7
Product Name Alternative
Inhibit, Inhibitor, EndogenousMetabolite, Endogenous Metabolite, 3Methyl2oxobutanoic acid, 3-Methyl-2-oxobutanoic acid, 2-Oxoisovaleric acid, 3 Methyl 2 oxobutanoic acid, alpha-Ketoisovaleric acid, a-Ketoisovaleric acid, α-Ketoisovaleric acid
Field of Research
Metabolism Research
Purity
95.00% (May vary between batches)
Solubility
10% DMSO+40% PEG300+5% Tween 80+45% Saline:2 mg/mL (17.22 mM) ; H2O:100 mg/mL (861.18 mM) ; DMSO:30 mg/mL (258.35 mM)
Smiles
CC (C) C (=O) C (O) =O
Molecular Formula
C5H8O3
Molecular Weight
116.12
Storage Conditions
-20°C
Notes
For research use only.
Available Sizes
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