BCKDHA Polyclonal Antibody
This is a BCKDHA Polyclonal Antibody from Reddot Biotech. This product is for Research Use Only.
Product Specifications
Background
The branched-chain alpha-keto acid (BCAA) dehydrogenase (BCKD) complex is an innter mitochondrial enzyme complex that catalyzes the second major step in the catabolism of the branched-chain amino acids leucine, isoleucine, and valine. The BCKD complex consists of three catalytic components: a heterotetrameric (alpha2-beta2) branched-chain alpha-keto acid decarboxylase (E1), a dihydrolipoyl transacylase (E2), and a dihydrolipoamide dehydrogenase (E3) . This gene encodes the alpha subunit of the decarboxylase (E1) component. Mutations in this gene result in maple syrup urine disease, type IA. Multiple transcript variants encoding different isoforms have been found for this gene.
Synonyms
BCKDHA, BCKDE1A, MSU, MSUD1, OVD1A, 2-oxoisovalerate dehydrogenase subunit alpha, mitochondrial
Gene ID
593
Swiss Prot
P12694
Reactivity
Human
Immunogen
Recombinant fusion protein of human BCKDHA
Clonality
Polyclonal
Conjugation
Unconjugated
Type
Polyclonal Antibody
Applications
WB, IF
Purification Method
Affinity purification
Assay Type
Antibody
Concentration
1mg/mL
Dilution
WB 1:500-1:2000, IF 1:50-1:200
Buffer
PBS with 0.02% sodium azide,50% glycerol, pH7.3.
Storage Conditions
Store at -20°C Valid for 12 months. Avoid freeze / thaw cycles.
Calculated Molecular Weight
22kDa/26kDa
Observed Molecular Weight
26KDa
Host or Source
Rabbit
Isotype
IgG
Available Sizes
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