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FXN/Frataxin Polyclonal Antibody

This is a FXN/Frataxin Polyclonal Antibody from Reddot Biotech. This product is for Research Use Only.

Product Specifications

Background

This nuclear gene encodes a mitochondrial protein which belongs to the FRATAXIN family. The protein functions in regulating mitochondrial iron transport and respiration. The expansion of intronic trinucleotide repeat GAA from 8-33 repeats to >90 repeats results in Friedreich ataxia. Alternative splicing results in multiple transcript variants.

Synonyms

FXN, CyaY, FA, FARR, FRDA, X25, frataxin

Gene ID

2395

Swiss Prot

Q16595

Reactivity

Human, Mouse

Immunogen

Recombinant fusion protein of human FXN / Frataxin

Clonality

Polyclonal

Conjugation

Unconjugated

Type

Polyclonal Antibody

Applications

IHC, IF

Purification Method

Affinity purification

Assay Type

Antibody

Concentration

1mg/mL

Dilution

IHC 1:50-1:100, IF 1:50-1:200

Buffer

PBS with 0.01% thiomersal,50% glycerol, pH7.3.

Storage Conditions

Store at -20°C Valid for 12 months. Avoid freeze / thaw cycles.

Calculated Molecular Weight

115kDa

Observed Molecular Weight

Refer to figures

Host or Source

Rabbit

Isotype

IgG

Available Sizes

Curated Selection

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