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ASS1 Polyclonal Antibody

This is a ASS1 Polyclonal Antibody from Reddot Biotech. This product is for Research Use Only.

Product Specifications

Background

ASS1 is a rate-limiting enzyme in the urea cycle. Citrullinemia type I is an autosomal recessive disorder that is caused by a deficiency of the urea cycle enzyme argininosuccinate synthetase (ASS1) . Deficiency of ASS1 shows various clinical manifestations encompassing severely affected patients with fatal neonatal hyperammonemia as well as asymptomatic individuals with only a biochemical phenotype.

Synonyms

Argininosuccinate synthase 1, Argininosuccinate synthase, Argininosuccinate synthetase 1, ASS, Ass-1, ass1, ASSA, ASSY, Citrulline aspartate ligase, Citrulline--aspartate ligase, CTLN1

Swiss Prot

P00966

Accession Number

BC021676

Reactivity

Human, Mouse, Rat

Immunogen

Fusion protein of human ASS1

Clonality

Polyclonal

Conjugation

Unconjugated

Type

Polyclonal Antibody

Applications

WB, IHC, ELISA

Purification Method

Antigen affinity purification

Assay Type

Antibody

Concentration

0.5 mg/mL

Dilution

WB 1:500-1:2000, IHC 1:25-1:100, ELISA 1:5000-1:10000

Buffer

PBS with 0.05% NaN3 and 40% Glycerol, pH7.4

Storage Conditions

Store at -20°C. Avoid freeze / thaw cycles.

Calculated Molecular Weight

47 kDa

Observed Molecular Weight

Refer to figures

Host or Source

Rabbit

Isotype

IgG

Available Sizes

Curated Selection

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