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Tiglyl carnitine (Standard)

Product Specifications

Product Name Alternative

BR-939

UNSPSC Description

Tiglyl carnitine (Standard) is the analytical standard of Tiglyl carnitine. This product is intended for research and analytical applications. Tiglyl carnitine is found to be associated with celiac disease and mitochondrial acetoacetyl-CoA thiolase (T2) deficiency.

Target Antigen

Endogenous Metabolite

Type

Reference Standards

Related Pathways

Metabolic Enzyme/Protease

Field of Research

Metabolic Disease

Assay Protocol

https://www.medchemexpress.com/tiglyl-carnitine-standard.html

Smiles

C/C=C(C)/C(O[C@H](CC([O-])=O)C[N+](C)(C)C)=O

Molecular Weight

243.30

References & Citations

[1]Fukao T, et al. The mitochondrial acetoacetyl-CoA thiolase (T2) deficiency in Japanese patients: urinary organic acid and blood acylcarnitine profiles under stable conditions have subtle abnormalities in T2-deficient patients with some residual T2 activity. J Inherit Metab Dis. 2003;26(5):423-31.

Shipping Conditions

Room temperature

Product Datasheet

http://file.medchemexpress.com/batch_PDF/HY-113408R/Tiglyl-carnitine-Standard-DataSheet-MedChemExpress.pdf

Product MSDS

http://file.medchemexpress.com/batch_PDF/HY-113408R/

CAS Number

64681-36-3

Available Sizes

Curated Selection

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