Tiglyl carnitine (Standard)

Tiglyl carnitine (Standard) is the analytical standard of Tiglyl carnitine. This product is intended for research and analytical applications. Tiglyl carnitine is found to be associated with celiac disease and mitochondrial acetoacetyl-CoA thiolase (T2) deficiency.

Product Specifications

CAS Number

[64681-36-3]

Product Name Alternative

BR-939

UNSPSC

12352211

Target

Endogenous Metabolite; Reference Standards

Type

Reference Standards

Related Pathways

Metabolic Enzyme/Protease; Others

Field of Research

Metabolic Disease

Assay Protocol

https://www.medchemexpress.com/tiglyl-carnitine-standard.html

Purity

98.01

Smiles

C/C=C(C)/C(O[C@H](CC([O-])=O)C[N+](C)(C)C)=O

Molecular Formula

C12H21NO4

Molecular Weight

243.30

References & Citations

[1]Fukao T, et al. The mitochondrial acetoacetyl-CoA thiolase (T2) deficiency in Japanese patients: urinary organic acid and blood acylcarnitine profiles under stable conditions have subtle abnormalities in T2-deficient patients with some residual T2 activity. J Inherit Metab Dis. 2003;26 (5) :423-31.