Ibiglustat
Product Specifications
CAS Number
1401090-53-6
Target
Transferase
Related Pathways
Metabolism
Purity
0.9914
Bioactivity
Ibiglustat (GZ402671) is a potent and selective Glucosylceramide synthase inhibitor and ceramide glucosyltransferase inhibitor. Ibiglustat blocks the formation of glucosylceramide (GL-1), a key intermediate in the synthesis of GL-3. Ibiglustat is potentially useful for treating Fabry disease. Fabry disease is a rare lysosomal storage disorder, which results in abnormal tissue deposits of a particular fatty substance called globotriaosylceramide (GL-3 or Gb3) throughout the body.
Smiles
CC(C)(NC(=O)O[C@@H]1CN2CCC1CC2)c1csc(n1)-c1ccc(F)cc1
Molecular Formula
C20H24FN3O2S
Molecular Weight
389.49
Shipping Conditions
Ice Packs
Storage Temperature
-20°C
Available Sizes
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