C17 Globotriaosylceramide (d18:1/17:0)

C17 Globotriaosylceramide (d18:1/17:0) is a sphygosine lipid that can be used to quantify Globotriaosylceramide in plasma and urine of patients with Fabry disease by gas chromatography-mass spectrometry (GC-MS) [1].

Product Specifications

CAS Number

[536745-81-0]

Product Name Alternative

Ceramide trihexoside (d18:1/17:0) ; Gb3 (d18:1) (C17:0)

UNSPSC

12352005

Target

Biochemical Assay Reagents

Type

Reference compound

Related Pathways

Others

Field of Research

Others

Assay Protocol

https://www.medchemexpress.com/c17-globotriaosylceramide-d18-1-17-0.html

Purity

99.0

Solubility

10 mM in DMSO

Smiles

OC[C@@H](O[C@H]([C@@H]([C@H]1O)O)O[C@@H]2[C@H](O[C@H]([C@@H]([C@H]2O)O)OC[C@@H]([C@H](O)/C=C/CCCCCCCCCCCCC)NC(CCCCCCCCCCCCCCCC)=O)CO)[C@@H]1O[C@H]3O[C@@H]([C@@H]([C@@H]([C@H]3O)O)O)CO

Molecular Formula

C53H99NO18

Molecular Weight

1038.35

References & Citations

[1]Provençal P, et al. Relative distribution of Gb3 isoforms/analogs in NOD/SCID/Fabry mice tissues determined by tandem mass spectrometry. Bioanalysis. 2016 Sep;8 (17) :1793-807.