Frataxin Recombinant Antibody / FXN
Frataxin is a nuclear-encoded mitochondrial protein implicated in Friedreich's ataxia (FRDA), a human autosomal recessive neurodegenerative disease. Lack of Frataxin causes iron to accumulate in the mitochondrial matrix suggesting that Frataxin is involved in mitochondrial iron homeostasis and possibly in iron transport. Frataxin has an alpha-beta fold consisting of two helices flanking an antiparallel beta sheet.
Product Specifications
UniProt
Q16595
Host
Mouse
Immunogen
Amino acids 57-210 from the human protein were used as the immunogen for this FXN antibody.
Clonality
Monoclonal
Isotype
IgG1 κ
Type
Recombinant
Applications
ELISA
Format
Purified
Buffer
1 mg/ml in 1X PBS; BSA free, sodium azide free
Reconstitution
Store the recombinant Frataxin antibody at 2-8oC (with azide) or aliquot and store at -20oC or colder (without azide).
Limitations
This recombinant Frataxin antibody is available for research use only.
CAS Number
9000-83-3
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DR3 (Death Receptor 3, DR-3, Apo-3, Apoptosis-inducing Receptor AIR, TRAMP, Death Domain Receptor 3, DDR3, Death Receptor beta, Lymphocyte Associated Receptor of Death, LARD, TR3, Translocating Chain Association Membrane Protein, Tumor Necrosis Factor Rec
