H-Abu-OH
Product Specifications
UNSPSC Description
H-Abu-OH, one of the three isomers of aminobutyric acid, is elevated in the plasma of children with with Reye's syndrome, tyrosinemia, homocystinuria, nonketotic hyperglycinemia, and ornithine transcarbamylase deficiency.
Target Antigen
Endogenous Metabolite
Type
Natural Products
Related Pathways
Metabolic Enzyme/Protease
Applications
Metabolism-protein/nucleotide metabolism
Field of Research
Metabolic Disease
Assay Protocol
https://www.medchemexpress.com/H-Abu-OH.html
Purity
98.0
Solubility
H2O : 50 mg/mL (ultrasonic)
Smiles
CC[C@H](N)C(O)=O
Molecular Weight
103.121
References & Citations
[1]Yudkoff M, et al. On the clinical significance of the plasma alpha-amino-n-butyric acid:leucine ratio. Am J Clin Nutr. 1979 Feb;32(2):282-5.
Shipping Conditions
Room Temperature
Storage Conditions
Store at room temperature 3 years
Product Datasheet
http://file.medchemexpress.com/batch_PDF/HY-W010589/H-Abu-OH-DataSheet-MedChemExpress.pdf
Product MSDS
http://file.medchemexpress.com/batch_PDF/HY-W010589/H-Abu-OH-SDS-MedChemExpress.pdf
Clinical Information
No Development Reported
CAS Number
1492-24-6
Available Sizes
Curated Selection
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